Диагностические критерии синдрома Бехчета
Описан в 1937 году турецким дерматологом Hulusi Behçet
International Study Group for Behçet’s Disease Criteria (1989)
Diagnosis requires: Recurrent oral ulceration: minor aphthous, major aphthous, or herpetiform ulceration observed by physician or by a reliable patient, with recurrence of 3 episodes in one I 2-month period
PLUS > 2/4 of the following:
I. Recurrent genital ulceration:
- aphthous ulceration or scarring, observed by physician or by a reliable patient
2. Eye lesions:
- anterior uveitis, or
- posterior uveits or
- cells in vitreous on slit lamp examination or
- retinal vasculitis observed by an ophthalmologist
3. Skin lesions:
- erythema nodosum, observed by physician or by a reliable patient or
- pseudofolliculitis, or
- papulopustular lesions; or
- acneiform nodules, observed by physician in post-adolescent patients not receiving corticosteroids
4. Positive pathergy test read by a physician at 24-48 hours:
- an indurated erythematous papulc or pustule that is> 2mm at the prick site after the application of a sterile needle or intradermal injection of saline
N.B. Findings applicable only in absence of other clinical explanations.
O’Duffy Behçet’s Disease Criteria (I974)
Diagnosis requires: Recurrent oral aphthous ulcers PLUS 2 of:
- Aphthous genital ulceration
- Uveitis
- Cutaneous “pustular” vasculitis
- Synovitis
- Meningoencephalitis
Incomplete form: Recurrent oral aphthous ulcers PLUS > 1 of above criteria Exclusions:herpes simplex infection, inflammatory bowel disease, Reiter’s syndrome and systemic lupus erythematosus (SLE)
Behçet’s Disease Research Committee of Japan Criteria (I972)
Diagnosis requires: All 4-Major Criteria
Major Criteria:
1. Recurrent aphthous ulceration in the mouth 2. Skin lesions
- Erythema nodosum-ilke eruptions
- Subcutaneous thromhophlebitis
- Hyperirritability of the skin
3. Eye lesions
- Recurrent hypopyon iritis or iridocyclitis
- Chorioretinitis
4. Genital ulcerations Incomplete type: 3/4 major criteria, or Recurrent hypopyon-iritis or typical chorioretinitis +1 other major criterion
Minor Criteria:
(Any number may present)
- Arthritis symptoms (arthralgia, swelling, erythema)
- Gastrointestinal lesions (e.g appen(licitis-like pains, melena)
- Epididymitis
- Vascular lesions (occlusion of blood vessels, aneurysms)
- Central nervous system involvement
- Brain stem syndrome
- Meningo-encephalomyelitic syndrome
- Confusional type